Fibrillin-1 (FBN1) (Marfan Syndrome Marker) Antibody, IgG1, Clone: [FBN1/6933], Mouse, Monoclonal
Artikelnummer:
NBT-2200-MSM3-P1
Produktübersicht
Artikelname:
Fibrillin-1 (FBN1) (Marfan Syndrome Marker) Antibody, IgG1, Clone: [FBN1/6933], Mouse, Monoclonal
Artikelnummer:
NBT-2200-MSM3-P1
Hersteller Artikelnummer:
2200-MSM3-P1
Alternativnummer:
NBT-2200-MSM3-P1-100
Hersteller:
NeoBiotechnologies
Wirt:
Mouse
Kategorie:
Antikörper
Applikation:
ELISA, IHC
Spezies Reaktivität:
Human
Immunogen:
Recombinant human Fibrillin 1 fragment around aa 330-476 (Exact sequence is proprietary)
Alternative Synonym:
350kDa glycoprotein component extracellular microfibril, ACMICD, FBN1, Fibrillin-15, Fibrillin-1, GPHYSD2, Marfan syndrome, MASS, MFS1, OCTD, SGS, SSKS, Weill Marchesani syndrome, WMS, WMS2
Produktbeschreibung
Fibrillin-1 is an extracellular matrix glycoprotein that serves as a structural component of calcium-binding microfibrils. These microfibrils provide force-bearing structural support in elastic and non-elastic connective tissue throughout the body.Mutations in this gene are associated with Marfan syndrome.
Produkteigenschaften
Klonalität:
Monoclonal
Klon-Bezeichnung:
[FBN1/6933]
Molekulargewicht:
350kDa
Isotyp:
IgG1
NCBI:
2200
UniProt:
P35555
Formulierung:
200ug/ml of Ab purified from Bioreactor Concentrate by Protein A/G. Prepared in 10mM PBS with 0.05% BSA & 0.05% azide. Also available WITHOUT BSA & azide at 1.0mg/ml.
Bilder
Formalin-fixed, paraffin-embedded human prostate stained with Fibr
Formalin-fixed, paraffin-embedded human kidney carcinoma stained with Fibrillin 1 Mouse Monoclonal Antibody (FBN1/6933). HIER: Tris/EDTA, pH9.0, 45min. 2°C: HRP-polymer, 30min. DAB, 5min.
Formalin-fixed, paraffin-embedded human prostate stained with Fibrillin 1 Mouse Monoclonal Antibody (FBN1/6933). HIER: Tris/EDTA, pH9.0, 45min. 2°C: HRP-polymer, 30min. DAB, 5min.
Formalin-fixed, paraffin-embedded human colon carcinoma stained with Fibrillin 1 Mouse Monoclonal Antibody (FBN1/6933). HIER: Tris/EDTA, pH9.0, 45min. 2°C: HRP-polymer, 30min. DAB, 5min.
SDS-PAGE Analysis of Purified Fibrillin 1 Mouse Monoclonal Antibody (FBN1/6933). Confirmation of Purity and Integrity of Antibody.