FA8A (light chain, Cleaved-Glu1668) Antibody, Rabbit, Polyclonal
Artikelnummer:
AST-L0450
- Bilder (0)
| Artikelname: | FA8A (light chain, Cleaved-Glu1668) Antibody, Rabbit, Polyclonal |
| Artikelnummer: | AST-L0450 |
| Hersteller Artikelnummer: | L0450 |
| Alternativnummer: | AST-L0450-50,AST-L0450-100 |
| Hersteller: | Assay Biotechnology |
| Wirt: | Rabbit |
| Kategorie: | Antikörper |
| Applikation: | ELISA, WB |
| Spezies Reaktivität: | Human, Mouse |
| Immunogen: | Synthesized peptide derived from human FA8A (light chain, Cleaved-Glu1668) |
| Alternative Synonym: | Coagulation factor VIII (Antihemophilic factor, AHF, Procoagulant component) [Cleaved into: Factor VIIIa heavy chain, 200 kDa isoform, Factor VIIIa heavy chain, 92 kDa isoform, Factor VIII B chain, Factor VIIIa light chain] |
| disease:Defects in F8 are the cause of hemophilia A (HEMA) [MIM:306700]. HEMA is a common recessive X-linked coagulation disorder. The frequency of hemophilia A is 1-2 in 10,000 male births in all ethnic groups. About 50% of patients have severe hemophil |
| Klonalität: | Polyclonal |
| UniProt: | P00451 |
| Quelle: | Polyclonal, Rabbit IgG |
| Reinheit: | The antibody was affinity-purified from rabbit serum by affinity-chromatography using specific immunogen. |
| Formulierung: | Liquid in PBS containing 50% glycerol, 0.5% BSA and 0.02% sodium azide. |
| Application Verdünnung: | WB 1:1000-2000 ELISA 1:5000-20000 |
